MALIGNANT PERIPHERAL NERVE SHEATH TUMOUR IN A 12 YEARS GIRL

A CASE REPORT

Authors

  • Samuel Seseja Dodoma Regional Referral Hospital, P.O.Box 904, Dodoma’ Tanzania.
  • Jeremiah Moshy MUHAS, P.O.Box 65014, Dar as Salaam’ Tanzania.

DOI:

https://doi.org/10.29309/TPMJ/2015.22.07.1229

Keywords:

malignant peripheral nerve sheath tumor, biological behavior, diagnostic challenges

Abstract

Malignant peripheral nerve sheath tumours (MPNSTs) are rare, aggressive soft
tissue sarcomas associated with poor prognosis, that most commonly affect patients aged
20 to 50 years, but have also been reported in children. The tumour is usually found in lower
extremities and only 10% to 20% of all lesions occur in head and neck region thus making it
a rare entity. Central involvement, particularly in the jawbones is quite unusual. There is little
reported in literature on these tumors in Africa. Here we report a rare case of intraosseous
MPNSTS occurring in the mandible in a 12-years old girl. The biological behavior and diagnostic
challenges of this rare malignancy are discussed.

Author Biographies

Samuel Seseja, Dodoma Regional Referral Hospital, P.O.Box 904, Dodoma’ Tanzania.

Department of Oral and Maxillofacial Surgery

Jeremiah Moshy, MUHAS, P.O.Box 65014, Dar as Salaam’ Tanzania.

Jeremiah Moshy
Department of Oral and Maxillofacial Surgery

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Published

2015-07-10

Issue

Vol. 22 No. 07 (2015): Vol: 22 No. 07

Section

Articles